Textbook of Cystic Fibrosis |
Common terms and phrases
abnormal absorption activity adults airway amylase antibiotics antibody Arch Dis Child associated bile acids bronchial bronchiectasis brosis calcium cells CF centers CF children CF patients CF serum Chapter children with cystic chronic ciliary Clin clinical cor pulmonale creatic Cystic Fibrosis Foundation cystic fibrosis patients decreased defect diabetes diagnosis dietary duct effect electrolytes Engl enzymes evaluation exocrine factor fatty acids fecal fibro Figure fluid genetic glands glucose glycoproteins growth hemoptysis heterozygotes hormone immune increased infants infection insulin intestinal lesions levels lipid liver lung disease malabsorption malnutrition meconium ileus metabolism mucus normal nutritional obstruction pancreatic pancreatic enzymes pancreatic insufficiency Pathol patients with CF patients with cystic Pediatr Pediatr Res plasma pneumothorax protein Pseudomonas aeruginosa pulmonary disease pulmonary function reported response Rev Respir saliva Sant'Agnese secretion secretory Shwachman H sodium sputum steatorrhea studies sweat test syndrome therapy tients tion tissue tocopherol tracheal